The first two years with hydranencephaly: an unusual medical course of a male child with a missing part of the brain

Stefan Bittmann 1

Abstract


Hydranencephaly is an extremely rare anomaly of cerebral structures that occurs in-utero. Cerebral hemispheres are destroyed with transformation into a membranous sac with cerebrospinal fluid and parts of cortex and white matter. The disorder has an incidence of 0.2% in children. Clinical symptoms in neonates are seizures, respiratory failure, flaccidity or decerebrate posturing. Complete absence of the cerebral hemispheres and falx are present. We present a case of a male newborn with hydranencephaly. A possible correlation with in utero exposure to vasoactive drugs will be discussed.


Keywords


Hydranencephaly; child; drug abuse

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References


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DOI: http://dx.doi.org/10.24294/jpedd.v2i2.978

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